Why is Hirschsprung disease common in male?

Hirschsprung’s disease is more common in males. Having other inherited conditions. Hirschsprung’s disease is associated with certain inherited conditions, such as Down syndrome and other abnormalities present at birth, such as congenital heart disease.

How do you treat Hirschsprung’s disease?

For most people, Hirschsprung’s disease is treated with surgery to bypass or remove the part of the colon that’s lacking nerve cells. There are two ways this can be done: a pull-through surgery or an ostomy surgery.

Is Hirschsprung disease life threatening?

Hirschsprung disease is a life-threatening illness, and treatment requires surgery. Children who have surgery for Hirschsprung disease most often feel better after surgery.

What does aganglionic megacolon mean in medical terms?

Aganglionic megacolon. Also called Hirschsprung’s disease, it is a congenital disorder of the colon in which nerve cells of the myenteric plexus in its walls, also known as ganglion cells, are absent.

What causes congenital aganglionic megacolon ( HSCR )?

Hirschsprung Disease: Congenital aganglionic megacolon Hirschsprung disease (HSCR) also called Congenital aganglionic megacolon is a motor disorder of the intestine, which is caused by the failure of neural crest cells to migrate completely during intestinal development during fetal life.

How to care for a child with aganglionic megacolon?

Nursing interventions for a child with aganglionic megacolon include: 1 Promote skin integrity. When performing routine colostomy care. 2 Promote comfort. Observe for signs of pain, such as crying, pulse and respiration rate increases,… 3 Maintain fluid balance. Accurate intake and output determinations and reporting the character,…

What are the signs and symptoms of megacolon?

External signs and symptoms are constipation of very long duration, abdominal bloating, abdominal tenderness and tympany, abdominal pain, palpation of hard fecal masses and, in toxic megacolon, fever, low blood potassium, tachycardia and may lead to shock.