Is HLHS worse than HRHS?

HRHS is less common than Hypoplastic Left Heart Syndrome (HLHS), which is an underdevelopment of the left side of the heart. If your doctor suspects a fetal heart anomaly after reviewing your routine ultrasound, he or she may request a fetal echocardiogram (echo), an ultrasound of the fetus’s heart.

How long do babies with HLHS live?

Most infants die within the first two weeks of life, with an average age at death of 4.5 days (31,33,34). Some patients with HLHS, however, can survive beyond sixty days, without any surgical intervention through the development of pulmonary hypertension (8,33).

What do you need to know about hypoplastic right heart syndrome?

Hypoplastic Right Heart Syndrome (HRHS) is a range of right-sided congenital heart defects in which the right-sided structures (tricuspid valve, right ventricle and/or pulmonary valve) are underdeveloped or not formed. When these structures are too small or do not function properly,…

When to have Glenn procedure for hypoplastic right heart syndrome?

In this surgery, the surgeon inserts an artificial tube to provide blood flow to the lungs. There is still mixing of oxygen poor and oxygen rich blood through the hole between the top chambers of the heart. Glenn Procedure: This procedure typically occurs between 4 and 6 months of age.

Can a baby with hypoplastic left heart syndrome go into shock?

“In a baby with hypoplastic left heart syndrome, if the natural connections between the heart’s left and right sides (foramen oval and ductus arteriosus) are allowed to close, he or she may go into shock.”. Signs of shock can include cool or clammy skin, a weak or rapid pulse, and dilated pupils.

How is the pulmonary artery repaired in hypoplastic right heart?

In a stage 1 Norwood procedure for hypoplastic right heart, the main pulmonary artery is separated from the left and right portions of the pulmonary artery and joined with the upper portion of the aorta. The proximal pulmonary artery is connected to the aortic arch, while the narrowed segment of the pulmonary trunk is repaired.