What is rubra pilaris?

Pityriasis rubra pilaris (PRP) is a rare condition that causes an orange-red, scaly rash on the skin with thickening and scaling of the palms and soles. There are often small scaly bumps surrounding the hair follicles, described as nutmeg grater.

Is Pityriasis rubra pilaris a form of psoriasis?

Pityriasis rubra pilaris (PRP) is a relatively uncommon skin disease, clinically characterized by follicular keratotic plugs, red to orange plaques, and palmoplantar hyperkeratosis. However, in cases with atypical clinical presentation, PRP is sometimes confused with psoriasis, both clinically and histopathologically.

Is Pityriasis genetic?

Familial pityriasis rubra pilaris usually has an autosomal dominant inheritance pattern , which means one copy of the altered gene in each cell is sufficient to cause the disorder. Affected individuals usually inherit the condition from one affected parent.

Is Pityriasis an autoimmune disease?

Although a virus is believed to cause pityriasis rosea, the disorder is not thought to be contagious. Some researchers have theorized that autoimmune factors may play a role in the development of pityriasis rosea. Autoimmunity is when the body’s immune system mistakenly attacks healthy tissue for unknown reasons.

What causes rubra?

The cause of pityriasis rubra pilaris is unknown. Atypical (nonclassic) forms exist in both age groups. Sunlight, HIV or another infection, minor trauma, or an autoimmune disorder may trigger a flare-up. Pityriasis rubra pilaris can manifest as hyperkeratotic yellowing of the palms and soles.

Is PRP an autoimmune disease?

The etiology of the disease remains unknown but several studies have reported an association of PRP with other autoimmune disorders [2-4].

Is Pityriasis Rosea a disability?

In a March 2009 rating action, the RO granted the Veteran’s claim of entitlement to service connection for a skin disorder of the feet, right arm, groin, and inner thighs, diagnosed as pityriasis rosea. The RO assigned a noncompensable disability rating, effective April 19, 2008.

Why did I get pityriasis rosea?

Pityriasis rosea is caused by a viral infection. The virus has recently been identified as one of the herpes viruses. Children and young adults are more susceptible, for reasons unknown. Recurrences are rare – a person who develops the skin rash has only a two per cent chance of experiencing it again.

Does Pityriasis rubra pilaris itch?

These patches are usually itchy. Initially, PRP patients may have the scaly patches only on some parts of the body. Patches most often occur on the elbows, knees, hands, feet, and ankles. Skin on the palms and soles may also become red or waxy and thickened with a classic orange hue (palmoplantar keratoderma).

What are the top 10 autoimmune diseases?

According to The Autoimmune Registry, the top 10 most common autoimmune diseases include:

• Rheumatoid arthritis.
• Hashimoto’s autoimmune thyroiditis.
• Celiac disease.
• Graves’ disease.
• Diabetes mellitus, type 1.
• Vitiligo.
• Rheumatic fever.
• Pernicious anemia/atrophic gastritis.

Does PRP cause itching?

For the most part, PRP can be itchy and uncomfortable. These symptoms can decrease over time, even if the rash looks like it’s getting worse. The condition usually doesn’t cause many complications. However, PRP Support Group notes that the rash can sometimes lead to other issues, such as ectropion.

What does pityriasis rubra pilaris do to the skin?

Pityriasis rubra pilaris. Pityriasis rubra pilaris (PRP) is a rare skin disorder that causes inflammation and scaling (exfoliation) of the skin. Causes. There are several subtypes of PRP. The cause is unknown, although genetic factors and an abnormal immune response may be involved.

Who was the first dermatologist to diagnose pityriasis rubra?

While Devergie saw the skin disorder as a combination of “follicular lesions and psoriasis palmaris, pityriasis capillitii and pityriasis rubra”, it would take yet another 21 years before another Frenchman and dermatologist by the name of Richaud to recognize PRP as a distinct entity.

Where did pityriasis rubra pilaris Nord get its name?

He was also the medical director of the St. Louis Hospital in Paris — the same hospital as Devergie.16 The name comes from three Latin words: pityriasis (scale-like), rubra (red) and pilaris (hair follicles).2 Like many rare disease, the PRP community laments the snail’s pace at which PRP research progresses.

What kind of skin disorder is pityriasis rosea?

Pityriasis rosea: Pityriasis rosea (PR) is a benign rash, a common skin disorder observed in otherwise healthy people, most frequently found in children and young adults, that is thought to be caused by a mild viral infection.