What is a double-chambered right ventricle?

A double-chambered right ventricle is a rare heart defect in which the right ventricle is separated into a high-pressure proximal and low-pressure distal chamber. This defect is considered to be congenital and typically presents in infancy or childhood but has been reported to present rarely in adults.

What does DCRV stand for?

Double-chambered right ventricle (DCRV) is a cardiac disease of the right ventricular outflow tract obstruction characterized by anomalous muscle bundles (AMB) that divide the right ventricle into two chambers, a high-pressure inflow chamber and a low-pressure outflow chamber.

What is a Perimembranous VSD?

Perimembranous ventricular septal defects (also called membranous VSD’S) are located in the membranous septum, a relatively small portion of the septum located near the heart valves. Ventricular septal defects may also be described as inlet or outlet VSDs. These terms further describe where the defect is located.

What causes a double chambered right ventricle?

Double Chambered Right Ventricle (DCRV) Double chambered right ventricle (DCRV) is a form of congenital heart disease in which the right ventricle is divided by anomalous muscle bundles into two chambers which causes subpulmonary stenosis in the region of the right ventricle and right ventricular outflow tract.

What happens to a child with a double outlet right ventricle?

Children born with a double outlet right ventricle heart defect always have another heart defect called a ventricular septal defect (VSD). This is a hole in the septum, the wall that divides the right and left ventricle. The VSD is actually helpful — it allows the child to live.

When do you need surgery for a double ventricle?

Double-outlet right ventricle. Some children will require surgery in the first few days after birth, and others may have surgery at a few months of age. Some people may have other associated congenital heart defects, including other holes in the heart (such as an atrial septal defect), heart valve problems or blood vessel problems.

Is there a hole between the left and right ventricles?

A hole also exists between the two ventricles (ventricular septal defect). In a normal heart, as shown on the left, the pulmonary artery connects to the right ventricle and the aorta connects to the left ventricle.